CASE REPORT
Mandibular odontogenic cysts associated with basal cell carcinoma in a patient with Gorlin-Goltz syndrome – Case Report
 
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1
Department of Maxillofacial Surgery. Medical University of Lublin, Poland
2
Medical University of Lublin, Poland
 
J Pre Clin Clin Res. 2018;12(3):95–99
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ABSTRACT:
Gorlin-Goltz syndrome (GGS) is a genetic disease of autosomal dominant inheritance. It is characterized by the presence of multiple basal-cell carcinoma foci, odontogenic keratocysts and anomalies of the skin, eyes, bones, nervous and endocrine system. Patients are predisposed to various neoplasms, such as medulloblastoma and fibrosarcoma. Rare incidence of the syndrome and multi-organ manifestations require providing patients with multi-specialist care, in particular, with dermatologists, dentists and surgeons. This is a case report of a 63-year-old patient with Gorlin-Goltz syndrome treated for odontogenic keratocysts of the mandible and basal-cell carcinoma. The report includes an extensive review of the GGS with regard to its etiology, features, clinical examination, diagnostic criteria and treatment modalities
CORRESPONDING AUTHOR:
Anna Gaweda   
Department of Maxillofacial Surgery. Medical University of Lublin, The Medical University of Lublin, Staszica 11, 20-081 Lublin, Poland, 20-081 Lublin, Poland
 
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